KMID : 0438520080150020176
|
|
Journal of the Korean Society of Neonatology 2008 Volume.15 No. 2 p.176 ~ p.182
|
|
A Case of Congenital Intrahepatic Portosystemic Shunt Associated with VSD Detected by Antenatal Sonography and Treated with Four Coil Embolizations and Open heart Surgery after Birth
|
|
Na Ji-Youn
Kim Sang-Duk Kim Ee-Kyung Choi Jung-Hwan Kim Han-Suk Kim Eun-Sun Chung Jin-Wook Cheon Jung-Eun
|
|
Abstract
|
|
|
A congenital portosystemic shunt is a very rare portosystemic vascular anomaly which leads to jaundice, hypoglycemia, hyperammonemia, liver cirrhosis, hepatic coma, and pulmonary hypertension. Anatomically, portosystemic shunts are divided into intra- and extra- hepatic shunts. Congenital intrahepatic portosystemic shunts are rare anomalies, and the early diagnosis is important to prevent hepatic encephalopathy and hypoglycemia. We report a case of an infant with symptoms of heart failure due to a congenital intrahepatic portosystemic shunt and a ventricular septal defect (VSD), which were treated successfully with four coil embolizations and open heart surgery for the VSD
|
|
KEYWORD
|
|
Congenital intrahepatic portosystemic shunt, Heart failure, Ventricular septal defect, Coil embolization
|
|
FullTexts / Linksout information
|
|
|
|
Listed journal information
|
|
|